{"_buckets": {"deposit": "edbea8f3-a7c5-456a-9e1a-c15714caa44d"}, "_deposit": {"id": "21178", "owners": [], "pid": {"revision_id": 0, "type": "depid", "value": "21178"}, "status": "published"}, "_oai": {"id": "oai:niigata-u.repo.nii.ac.jp:00021178"}, "item_7_alternative_title_1": {"attribute_name": "\u305d\u306e\u4ed6\u306e\u30bf\u30a4\u30c8\u30eb", "attribute_value_mlt": [{"subitem_alternative_title": "Brain CT and MRI Findings in Kearns-Sayre Syndrome"}]}, "item_7_biblio_info_6": {"attribute_name": "\u66f8\u8a8c\u60c5\u5831", "attribute_value_mlt": [{"bibliographicIssueDates": {"bibliographicIssueDate": "1992-01", "bibliographicIssueDateType": "Issued"}, "bibliographicIssueNumber": "1", "bibliographicPageEnd": "53", "bibliographicPageStart": "49", "bibliographicVolumeNumber": "106", "bibliographic_titles": [{"bibliographic_title": "\u65b0\u6f5f\u533b\u5b66\u4f1a\u96d1\u8a8c"}, {"bibliographic_title": "\u65b0\u6f5f\u533b\u5b66\u4f1a\u96d1\u8a8c", "bibliographic_titleLang": "en"}]}]}, "item_7_description_4": {"attribute_name": "\u6284\u9332", "attribute_value_mlt": [{"subitem_description": "Kearns-Sayre syndrome (KSS) is a subgroup of the mitochondrial encephalomyopathy whose main features are ophthalmoplegia, retinal pigmentary degeneration, heart conduction block with other minor neurological disorders. The most common neuropathological findings for this disorder is spongy degeneration in the white matter of the brain. In this study, we examined the neurological findings and the brain CT or MRI of our seven patients with KSS. CT and MRI revealed cerebral cortical atrophy in five of seven patients with mental deterioration and abnormal intensity lesions in the basal ganglia, midbrain and cerebral and cerebellar white matter of one patient who showed episodic unconsciousness due to lactic acidosis. Neurological and MRI findings differ quantitatively and qualitatively between patients with KSS.", "subitem_description_type": "Abstract"}]}, "item_7_full_name_3": {"attribute_name": "\u8457\u8005\u5225\u540d", "attribute_value_mlt": [{"nameIdentifiers": [{"nameIdentifier": "129837", "nameIdentifierScheme": "WEKO"}], "names": [{"name": "Jing, Xu"}]}, {"nameIdentifiers": [{"nameIdentifier": "129838", "nameIdentifierScheme": "WEKO"}], "names": [{"name": "Tanaka, Keiko"}]}, {"nameIdentifiers": [{"nameIdentifier": "129839", "nameIdentifierScheme": "WEKO"}], "names": [{"name": "Tanno, Yoshinori"}]}, {"nameIdentifiers": [{"nameIdentifier": "129840", "nameIdentifierScheme": "WEKO"}], "names": [{"name": "Yuasa, Tatsuhiko"}]}]}, "item_7_publisher_7": {"attribute_name": "\u51fa\u7248\u8005", "attribute_value_mlt": [{"subitem_publisher": "\u65b0\u6f5f\u533b\u5b66\u4f1a"}]}, "item_7_select_19": {"attribute_name": "\u8457\u8005\u7248\u30d5\u30e9\u30b0", "attribute_value_mlt": [{"subitem_select_item": "publisher"}]}, "item_7_source_id_11": {"attribute_name": "\u66f8\u8a8c\u30ec\u30b3\u30fc\u30c9ID", "attribute_value_mlt": [{"subitem_source_identifier": "AN00182415", "subitem_source_identifier_type": "NCID"}]}, "item_7_source_id_9": {"attribute_name": "ISSN", "attribute_value_mlt": [{"subitem_source_identifier": "00290440", "subitem_source_identifier_type": "ISSN"}]}, "item_creator": {"attribute_name": "\u8457\u8005", "attribute_type": "creator", "attribute_value_mlt": [{"creatorNames": [{"creatorName": "\u8a31, \u6676"}], "nameIdentifiers": [{"nameIdentifier": "129833", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "\u7530\u4e2d, \u6075\u5b50"}], "nameIdentifiers": [{"nameIdentifier": "129834", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "\u4e39\u91ce, \u82b3\u7bc4"}], "nameIdentifiers": [{"nameIdentifier": "129835", "nameIdentifierScheme": "WEKO"}]}, {"creatorNames": [{"creatorName": "\u6e6f\u6d45, \u9f8d\u5f66"}], "nameIdentifiers": [{"nameIdentifier": "129836", "nameIdentifierScheme": "WEKO"}]}]}, "item_files": {"attribute_name": "\u30d5\u30a1\u30a4\u30eb\u60c5\u5831", "attribute_type": "file", "attribute_value_mlt": [{"accessrole": "open_date", "date": [{"dateType": "Available", "dateValue": "2019-08-16"}], "displaytype": "detail", "download_preview_message": "", "file_order": 0, "filename": "106(01)_49-53.pdf", "filesize": [{"value": "1.8 MB"}], "format": "application/pdf", "future_date_message": "", "is_thumbnail": false, "licensetype": "license_free", "mimetype": "application/pdf", "size": 1800000.0, "url": {"label": "106(01)_49-53.pdf", "url": "https://niigata-u.repo.nii.ac.jp/record/21178/files/106(01)_49-53.pdf"}, "version_id": "37fb1f96-8559-4c9d-a6c6-1648a5a21e8b"}]}, "item_keyword": {"attribute_name": "\u30ad\u30fc\u30ef\u30fc\u30c9", "attribute_value_mlt": [{"subitem_subject": "Kearns-Sayre syndrome", "subitem_subject_scheme": "Other"}, {"subitem_subject": "brain CT", "subitem_subject_scheme": "Other"}, {"subitem_subject": "MRI", "subitem_subject_scheme": "Other"}, {"subitem_subject": "cerebral and cerebellar cortical atrophy", "subitem_subject_scheme": "Other"}, {"subitem_subject": "\u30df\u30c8\u30b3\u30f3\u30c9\u30ea\u30a2\u8133\u7b4b\u75c7", "subitem_subject_scheme": "Other"}, {"subitem_subject": "\u982d\u90e8CT", "subitem_subject_scheme": "Other"}, {"subitem_subject": "\u5927\u8133\u30fb\u5c0f\u8133\u76ae\u8cea\u840e\u7e2e", "subitem_subject_scheme": "Other"}]}, "item_language": {"attribute_name": "\u8a00\u8a9e", "attribute_value_mlt": [{"subitem_language": "jpn"}]}, "item_resource_type": {"attribute_name": "\u8cc7\u6e90\u30bf\u30a4\u30d7", "attribute_value_mlt": [{"resourcetype": "departmental bulletin paper", "resourceuri": "http://purl.org/coar/resource_type/c_6501"}]}, "item_title": "Kearns-Sayre\u75c7\u5019\u7fa4\u306e\u4e2d\u67a2\u795e\u7d4c\u753b\u50cf\u6240\u898b", "item_titles": {"attribute_name": "\u30bf\u30a4\u30c8\u30eb", "attribute_value_mlt": [{"subitem_title": "Kearns-Sayre\u75c7\u5019\u7fa4\u306e\u4e2d\u67a2\u795e\u7d4c\u753b\u50cf\u6240\u898b"}, {"subitem_title": "Kearns-Sayre\u75c7\u5019\u7fa4\u306e\u4e2d\u67a2\u795e\u7d4c\u753b\u50cf\u6240\u898b", "subitem_title_language": "en"}]}, "item_type_id": "7", "owner": "1", "path": ["453/456", "471/537/538/1178"], "permalink_uri": "http://hdl.handle.net/10191/39495", "pubdate": {"attribute_name": "\u516c\u958b\u65e5", "attribute_value": "2016-03-14"}, "publish_date": "2016-03-14", "publish_status": "0", "recid": "21178", "relation": {}, "relation_version_is_last": true, "title": ["Kearns-Sayre\u75c7\u5019\u7fa4\u306e\u4e2d\u67a2\u795e\u7d4c\u753b\u50cf\u6240\u898b"], "weko_shared_id": null}