{"created":"2021-03-01T06:26:12.188293+00:00","id":21178,"links":{},"metadata":{"_buckets":{"deposit":"edbea8f3-a7c5-456a-9e1a-c15714caa44d"},"_deposit":{"id":"21178","owners":[],"pid":{"revision_id":0,"type":"depid","value":"21178"},"status":"published"},"_oai":{"id":"oai:niigata-u.repo.nii.ac.jp:00021178","sets":["453:456","471:537:538:1178"]},"item_7_alternative_title_1":{"attribute_name":"その他のタイトル","attribute_value_mlt":[{"subitem_alternative_title":"Brain CT and MRI Findings in Kearns-Sayre Syndrome"}]},"item_7_biblio_info_6":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"1992-01","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1","bibliographicPageEnd":"53","bibliographicPageStart":"49","bibliographicVolumeNumber":"106","bibliographic_titles":[{"bibliographic_title":"新潟医学会雑誌"},{"bibliographic_title":"新潟医学会雑誌","bibliographic_titleLang":"en"}]}]},"item_7_description_4":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"Kearns-Sayre syndrome (KSS) is a subgroup of the mitochondrial encephalomyopathy whose main features are ophthalmoplegia, retinal pigmentary degeneration, heart conduction block with other minor neurological disorders. The most common neuropathological findings for this disorder is spongy degeneration in the white matter of the brain. In this study, we examined the neurological findings and the brain CT or MRI of our seven patients with KSS. CT and MRI revealed cerebral cortical atrophy in five of seven patients with mental deterioration and abnormal intensity lesions in the basal ganglia, midbrain and cerebral and cerebellar white matter of one patient who showed episodic unconsciousness due to lactic acidosis. Neurological and MRI findings differ quantitatively and qualitatively between patients with KSS.","subitem_description_type":"Abstract"}]},"item_7_full_name_3":{"attribute_name":"著者別名","attribute_value_mlt":[{"nameIdentifiers":[{"nameIdentifier":"129837","nameIdentifierScheme":"WEKO"}],"names":[{"name":"Jing, Xu"}]},{"nameIdentifiers":[{"nameIdentifier":"129838","nameIdentifierScheme":"WEKO"}],"names":[{"name":"Tanaka, Keiko"}]},{"nameIdentifiers":[{"nameIdentifier":"129839","nameIdentifierScheme":"WEKO"}],"names":[{"name":"Tanno, Yoshinori"}]},{"nameIdentifiers":[{"nameIdentifier":"129840","nameIdentifierScheme":"WEKO"}],"names":[{"name":"Yuasa, Tatsuhiko"}]}]},"item_7_publisher_7":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"新潟医学会"}]},"item_7_select_19":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_select_item":"publisher"}]},"item_7_source_id_11":{"attribute_name":"書誌レコードID","attribute_value_mlt":[{"subitem_source_identifier":"AN00182415","subitem_source_identifier_type":"NCID"}]},"item_7_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"00290440","subitem_source_identifier_type":"ISSN"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"許, 晶"}],"nameIdentifiers":[{"nameIdentifier":"129833","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"田中, 恵子"}],"nameIdentifiers":[{"nameIdentifier":"129834","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"丹野, 芳範"}],"nameIdentifiers":[{"nameIdentifier":"129835","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"湯浅, 龍彦"}],"nameIdentifiers":[{"nameIdentifier":"129836","nameIdentifierScheme":"WEKO"}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2019-08-16"}],"displaytype":"detail","filename":"106(01)_49-53.pdf","filesize":[{"value":"1.8 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"106(01)_49-53.pdf","url":"https://niigata-u.repo.nii.ac.jp/record/21178/files/106(01)_49-53.pdf"},"version_id":"37fb1f96-8559-4c9d-a6c6-1648a5a21e8b"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"Kearns-Sayre syndrome","subitem_subject_scheme":"Other"},{"subitem_subject":"brain CT","subitem_subject_scheme":"Other"},{"subitem_subject":"MRI","subitem_subject_scheme":"Other"},{"subitem_subject":"cerebral and cerebellar cortical atrophy","subitem_subject_scheme":"Other"},{"subitem_subject":"ミトコンドリア脳筋症","subitem_subject_scheme":"Other"},{"subitem_subject":"頭部CT","subitem_subject_scheme":"Other"},{"subitem_subject":"大脳・小脳皮質萎縮","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"departmental bulletin paper","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"Kearns-Sayre症候群の中枢神経画像所見","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"Kearns-Sayre症候群の中枢神経画像所見"},{"subitem_title":"Kearns-Sayre症候群の中枢神経画像所見","subitem_title_language":"en"}]},"item_type_id":"7","owner":"1","path":["456","1178"],"pubdate":{"attribute_name":"公開日","attribute_value":"2016-03-14"},"publish_date":"2016-03-14","publish_status":"0","recid":"21178","relation_version_is_last":true,"title":["Kearns-Sayre症候群の中枢神経画像所見"],"weko_creator_id":"1","weko_shared_id":null},"updated":"2022-12-15T04:18:05.122781+00:00"}