@article{oai:niigata-u.repo.nii.ac.jp:00021178,
 author = {許, 晶 and 田中, 恵子 and 丹野, 芳範 and 湯浅, 龍彦},
 issue = {1},
 journal = {新潟医学会雑誌, 新潟医学会雑誌},
 month = {Jan},
 note = {Kearns-Sayre syndrome (KSS) is a subgroup of the mitochondrial encephalomyopathy whose main features are ophthalmoplegia, retinal pigmentary degeneration, heart conduction block with other minor neurological disorders. The most common neuropathological findings for this disorder is spongy degeneration in the white matter of the brain. In this study, we examined the neurological findings and the brain CT or MRI of our seven patients with KSS. CT and MRI revealed cerebral cortical atrophy in five of seven patients with mental deterioration and abnormal intensity lesions in the basal ganglia, midbrain and cerebral and cerebellar white matter of one patient who showed episodic unconsciousness due to lactic acidosis. Neurological and MRI findings differ quantitatively and qualitatively between patients with KSS.},
 pages = {49--53},
 title = {Kearns-Sayre症候群の中枢神経画像所見},
 volume = {106},
 year = {1992}
}