{"_buckets": {"deposit": "5533262c-94b3-4c04-9629-098f0ea2a954"}, "_deposit": {"id": "25537", "owners": [], "pid": {"revision_id": 0, "type": "depid", "value": "25537"}, "status": "published"}, "_oai": {"id": "oai:niigata-u.repo.nii.ac.jp:00025537"}, "item_7_alternative_title_1": {"attribute_name": "\u305d\u306e\u4ed6\u306e\u30bf\u30a4\u30c8\u30eb", "attribute_value_mlt": [{"subitem_alternative_title": "A case of oral self-mutilation in Lesch-Nyhan syndrome"}]}, "item_7_biblio_info_6": {"attribute_name": "\u66f8\u8a8c\u60c5\u5831", "attribute_value_mlt": [{"bibliographicIssueDates": {"bibliographicIssueDate": "2007-07", "bibliographicIssueDateType": "Issued"}, "bibliographicIssueNumber": "1", "bibliographicPageEnd": "35", "bibliographicPageStart": "31", "bibliographicVolumeNumber": "37", "bibliographic_titles": [{"bibliographic_title": "\u65b0\u6f5f\u6b6f\u5b66\u4f1a\u96d1\u8a8c"}, {"bibliographic_title": "\u65b0\u6f5f\u6b6f\u5b66\u4f1a\u96d1\u8a8c", "bibliographic_titleLang": "en"}]}]}, "item_7_description_4": {"attribute_name": "\u6284\u9332", "attribute_value_mlt": [{"subitem_description": "Lesch-Nyhan syndrome is a rare inborn error of purine metabolism caused of lack of hypoxanthine-guanine phosphoribosyl transferase (HGPRT), and is characterized by involuntary moments, mental retardation, cerebral palsy, and self-injurious behavior. Self-mutilation to lips and fingers are often observed, and prevention of self-mutilation and treatment to the destruction raise significant difficulties. We treated an 8 year-old boy with Lesch-Nyhan syndrome who had severe lower lip injuries with self-mutilation. The patient\u0027s central and lateral lower incisors were covered by resin at his first visit, and then treated by crown amputation and pulpectomy under general anesthesia. We also corrected form of his lower lip which was deeply wounded with self-mutilation. His self-injurious behavior is not seen for ten months after the treatment, but more follow-up examination is needed, as there are some reports that self-mutilation had restarted after the treatment.", "subitem_description_type": "Abstract"}, {"subitem_description": "Lesch-Nyhan\u75c7\u5019\u7fa4\u306fhypoxanthine-guanine phosphoribosyl transferase (HGPRT) \u306e\u6b20\u640d\u306b\u3088\u308a\u30d7\u30ea\u30f3\u4f53\u4ee3\u8b1d\u306e\u7570\u5e38\u3092\u304d\u305f\u3059\u7a00\u306a\u5148\u5929\u6027\u306e\u75be\u60a3\u3067\u3042\u308a, \u5c0f\u5150\u671f\u306b\u767a\u75c7\u3057, \u4e0d\u968f\u610f\u904b\u52d5, \u7cbe\u795e\u767a\u9054\u9045\u6ede, \u8133\u6027\u9ebb\u75fa, \u81ea\u50b7\u884c\u70ba\u306a\u3069\u306e\u7279\u5fb4\u7684\u306a\u81e8\u5e8a\u50cf\u3092\u5448\u3059\u308b\u75be\u60a3\u3067\u3042\u308b\u3002\u81ea\u50b7\u884c\u70ba\u306f\u53e3\u5507\u3084\u624b\u6307\u306b\u591a\u304f\u307f\u3089\u308c, 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