{"_buckets": {"deposit": "d30016f2-f0cd-4e10-8b85-3aaa19277d9a"}, "_deposit": {"id": "24380", "owners": [], "pid": {"revision_id": 0, "type": "depid", "value": "24380"}, "status": "published"}, "_oai": {"id": "oai:niigata-u.repo.nii.ac.jp:00024380"}, "item_7_alternative_title_1": {"attribute_name": "\u305d\u306e\u4ed6\u306e\u30bf\u30a4\u30c8\u30eb", "attribute_value_mlt": [{"subitem_alternative_title": "Machado-Joseph disease : Diagnostic criteria for Japanese cases(Hereditary Spinocerebellar Degeneration : recent advances)"}]}, "item_7_biblio_info_6": {"attribute_name": "\u66f8\u8a8c\u60c5\u5831", "attribute_value_mlt": [{"bibliographicIssueDates": {"bibliographicIssueDate": "1986-12", "bibliographicIssueDateType": "Issued"}, "bibliographicIssueNumber": "12", "bibliographicPageEnd": "714", "bibliographicPageStart": "709", "bibliographicVolumeNumber": "100", "bibliographic_titles": [{"bibliographic_title": "\u65b0\u6f5f\u533b\u5b66\u4f1a\u96d1\u8a8c"}, {"bibliographic_title": "\u65b0\u6f5f\u533b\u5b66\u4f1a\u96d1\u8a8c", "bibliographic_titleLang": "en"}]}]}, "item_7_description_4": {"attribute_name": "\u6284\u9332", "attribute_value_mlt": [{"subitem_description": "Machado-Joseph disease\uff08MJD\uff09is an autosomal dominant hereditary ataxia found among descendants of Portuguese from the Azores Islands. Two black families and one Indian family were reported as having MJD, although no pathological investigation had done in those families. Sakai et al. and Yuasa et al. also described Japanese cases whose clinical and pathological findings were compatible with those of MJD in Portuguese. Four other Japanese cases, reported by wakabayashi et al., Mizutani et al. and Ikeda et al., were thought to be classified in Japanese MJD both clinical and pathological point of view. Recently Barbeau et al. proposed diagnostic criteria, modification of the one of Lima and Coutinho, for MJD. Though the criteria are sufficient for Caucasian patients among descendants of Portuguese, it seem to be necessary new criteria for especially Japanese patients. We have proposed here a guideline for diagnosis of MJD in Japanese cases: which consist of three diagnostic levels; clinical suspect, clinico-pathologic diagnostic and clinico-pathologico-biochemical diagnostic level\uff08Table 3\uff09. The criteria proposed here should be revised later when more cases would be examined clinically and pathologically.", "subitem_description_type": "Abstract"}]}, "item_7_full_name_3": {"attribute_name": "\u8457\u8005\u5225\u540d", "attribute_value_mlt": [{"nameIdentifiers": [{"nameIdentifier": "145719", "nameIdentifierScheme": "WEKO"}], "names": [{"name": "Yuasa, Tatsuhiko"}]}]}, "item_7_publisher_7": {"attribute_name": "\u51fa\u7248\u8005", "attribute_value_mlt": [{"subitem_publisher": "\u65b0\u6f5f\u533b\u5b66\u4f1a"}]}, "item_7_select_19": {"attribute_name": "\u8457\u8005\u7248\u30d5\u30e9\u30b0", "attribute_value_mlt": [{"subitem_select_item": "publisher"}]}, "item_7_source_id_11": {"attribute_name": "\u66f8\u8a8c\u30ec\u30b3\u30fc\u30c9ID", "attribute_value_mlt": [{"subitem_source_identifier": "AN00182415", "subitem_source_identifier_type": "NCID"}]}, "item_7_source_id_9": {"attribute_name": "ISSN", "attribute_value_mlt": [{"subitem_source_identifier": "00290440", "subitem_source_identifier_type": "ISSN"}]}, "item_creator": {"attribute_name": "\u8457\u8005", "attribute_type": "creator", "attribute_value_mlt": [{"creatorNames": [{"creatorName": "\u6e6f\u6d45, \u9f8d\u5f66"}], "nameIdentifiers": [{"nameIdentifier": "145718", "nameIdentifierScheme": "WEKO"}]}]}, "item_files": {"attribute_name": "\u30d5\u30a1\u30a4\u30eb\u60c5\u5831", "attribute_type": "file", "attribute_value_mlt": [{"accessrole": "open_date", "date": [{"dateType": "Available", "dateValue": "2019-08-19"}], "displaytype": "detail", "download_preview_message": "", "file_order": 0, "filename": "100(12)_709-714.pdf", "filesize": [{"value": "496.6 kB"}], "format": "application/pdf", "future_date_message": "", "is_thumbnail": false, "licensetype": "license_free", "mimetype": "application/pdf", "size": 496600.0, "url": {"label": "100(12)_709-714.pdf", "url": "https://niigata-u.repo.nii.ac.jp/record/24380/files/100(12)_709-714.pdf"}, "version_id": "1af4b294-ccdc-4b0d-a39d-2fb2ecd87fef"}]}, "item_keyword": {"attribute_name": "\u30ad\u30fc\u30ef\u30fc\u30c9", "attribute_value_mlt": [{"subitem_subject": "Machado-Joseph disease", "subitem_subject_scheme": "Other"}, {"subitem_subject": "Marie\u0027s ataxia", "subitem_subject_scheme": "Other"}]}, "item_language": {"attribute_name": "\u8a00\u8a9e", "attribute_value_mlt": [{"subitem_language": "jpn"}]}, "item_resource_type": {"attribute_name": "\u8cc7\u6e90\u30bf\u30a4\u30d7", "attribute_value_mlt": [{"resourcetype": "departmental bulletin paper", "resourceuri": "http://purl.org/coar/resource_type/c_6501"}]}, "item_title": "1) Machado-Joseph disease : Japanese type; \u8a3a\u65ad\u306e\u305f\u3081\u306e\u30ac\u30a4\u30c9\u30e9\u30a4\u30f3(\u30b7\u30f3\u30dd\u30b8\u30a6\u30e0 \u907a\u4f1d\u6027\u810a\u9ac4\u5c0f\u8133\u5909\u6027\u75c7 : \u6700\u8fd1\u306e\u77e5\u898b\u304b\u3089, \u7b2c417\u56de\u65b0\u6f5f\u533b\u5b66\u4f1a)", "item_titles": {"attribute_name": "\u30bf\u30a4\u30c8\u30eb", "attribute_value_mlt": [{"subitem_title": "1) Machado-Joseph disease : Japanese type; \u8a3a\u65ad\u306e\u305f\u3081\u306e\u30ac\u30a4\u30c9\u30e9\u30a4\u30f3(\u30b7\u30f3\u30dd\u30b8\u30a6\u30e0 \u907a\u4f1d\u6027\u810a\u9ac4\u5c0f\u8133\u5909\u6027\u75c7 : \u6700\u8fd1\u306e\u77e5\u898b\u304b\u3089, \u7b2c417\u56de\u65b0\u6f5f\u533b\u5b66\u4f1a)"}, {"subitem_title": "1) Machado-Joseph disease : Japanese type; \u8a3a\u65ad\u306e\u305f\u3081\u306e\u30ac\u30a4\u30c9\u30e9\u30a4\u30f3(\u30b7\u30f3\u30dd\u30b8\u30a6\u30e0 \u907a\u4f1d\u6027\u810a\u9ac4\u5c0f\u8133\u5909\u6027\u75c7 : \u6700\u8fd1\u306e\u77e5\u898b\u304b\u3089, \u7b2c417\u56de\u65b0\u6f5f\u533b\u5b66\u4f1a)", "subitem_title_language": "en"}]}, "item_type_id": "7", "owner": "1", "path": ["453/456", "471/537/538/1239"], "permalink_uri": "http://hdl.handle.net/10191/35759", "pubdate": {"attribute_name": "\u516c\u958b\u65e5", "attribute_value": "2015-12-16"}, "publish_date": "2015-12-16", "publish_status": "0", "recid": "24380", "relation": {}, "relation_version_is_last": true, "title": ["1) Machado-Joseph disease : Japanese type; \u8a3a\u65ad\u306e\u305f\u3081\u306e\u30ac\u30a4\u30c9\u30e9\u30a4\u30f3(\u30b7\u30f3\u30dd\u30b8\u30a6\u30e0 \u907a\u4f1d\u6027\u810a\u9ac4\u5c0f\u8133\u5909\u6027\u75c7 : \u6700\u8fd1\u306e\u77e5\u898b\u304b\u3089, \u7b2c417\u56de\u65b0\u6f5f\u533b\u5b66\u4f1a)"], "weko_shared_id": null}