@article{oai:niigata-u.repo.nii.ac.jp:00024383, author = {高橋, 均 and 武田, 茂樹 and 大浜, 栄作 and 生田, 房弘 and 本間, 義章}, issue = {12}, journal = {新潟医学会雑誌, 新潟医学会雑誌}, month = {Dec}, note = {Two autopsied cases, a 66-year-old man and a 65-year-old woman, from different families on Sado with dominantly inherited progressive cerebellar ataxia were described. Total clinical courses were 36 and 11 years respectively, Neuropathologically, both were characterized by marked degeneration and loss of Purkinje cells in the cerebellar cortex and of neurons in the inferior olive, being diagnosed as cerebello-olivary atrophy of Holmes type. In the former, however, the peripheral sensory nervous systems and their ascending tracts in the spinal cord were also involved. The neuropathological findings of these cases were discussed with a review of literature.}, pages = {725--732}, title = {4) 遺伝性失調症 : Holmes型小脳萎縮症の2剖検例(シンポジウム 遺伝性脊髄小脳変性症 : 最近の知見から, 第417回新潟医学会)}, volume = {100}, year = {1986} }