{"created":"2021-03-01T06:28:36.470406+00:00","id":23360,"links":{},"metadata":{"_buckets":{"deposit":"56206602-fdf6-4f92-b1ff-e4a3d804ad25"},"_deposit":{"id":"23360","owners":[],"pid":{"revision_id":0,"type":"depid","value":"23360"},"status":"published"},"_oai":{"id":"oai:niigata-u.repo.nii.ac.jp:00023360","sets":["453:456","471:537:538:1219"]},"item_7_alternative_title_1":{"attribute_name":"その他のタイトル","attribute_value_mlt":[{"subitem_alternative_title":"Congenital Metabolic Diseases as Perinatal Disorders(Current Care and Problems in Perinatal Period)"}]},"item_7_biblio_info_6":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"1988-08","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"8","bibliographicPageEnd":"470","bibliographicPageStart":"466","bibliographicVolumeNumber":"102","bibliographic_titles":[{"bibliographic_title":"新潟医学会雑誌"},{"bibliographic_title":"新潟医学会雑誌","bibliographic_titleLang":"en"}]}]},"item_7_description_4":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"More than 350 kinds of congenital metabolic diseases are described in the pediatric textbook by Nelson. During the past fifteen years, we have found 81 patients with 15 kinds of congenital metabolic diseases. In these 81 patients, only 3 patients (congenital urea cycle enzyme deficiency and galactosemia) presented with abnormal signs and symptoms such as vomiting, failure to thrive or hyperammonemia in perinatal period. Although the incidence of congenital metabolic diseases presenting with abnormal signs and symptoms early in perinatal period is very low, early detection and treatment are important for preventing fatal outcome or abnormal neurological sequeles.","subitem_description_type":"Abstract"}]},"item_7_full_name_3":{"attribute_name":"著者別名","attribute_value_mlt":[{"nameIdentifiers":[{"nameIdentifier":"140778","nameIdentifierScheme":"WEKO"}],"names":[{"name":"Asami, Tadashi"}]},{"nameIdentifiers":[{"nameIdentifier":"140779","nameIdentifierScheme":"WEKO"}],"names":[{"name":"Matsui, Toshiharu"}]},{"nameIdentifiers":[{"nameIdentifier":"140780","nameIdentifierScheme":"WEKO"}],"names":[{"name":"Suda, Masashi"}]}]},"item_7_publisher_7":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"新潟医学会"}]},"item_7_select_19":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_select_item":"publisher"}]},"item_7_source_id_11":{"attribute_name":"書誌レコードID","attribute_value_mlt":[{"subitem_source_identifier":"AN00182415","subitem_source_identifier_type":"NCID"}]},"item_7_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"00290440","subitem_source_identifier_type":"ISSN"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"浅見, 直"}],"nameIdentifiers":[{"nameIdentifier":"140775","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"松井, 俊晴"}],"nameIdentifiers":[{"nameIdentifier":"140776","nameIdentifierScheme":"WEKO"}]},{"creatorNames":[{"creatorName":"須田, 昌司"}],"nameIdentifiers":[{"nameIdentifier":"140777","nameIdentifierScheme":"WEKO"}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2019-08-19"}],"displaytype":"detail","filename":"102(8)_466-470.pdf","filesize":[{"value":"1.0 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"102(8)_466-470.pdf","url":"https://niigata-u.repo.nii.ac.jp/record/23360/files/102(8)_466-470.pdf"},"version_id":"1fc881c7-d9d5-4ddd-bdb2-9a2e1dce07fb"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"congenital metabolic disease","subitem_subject_scheme":"Other"},{"subitem_subject":"galactosemia","subitem_subject_scheme":"Other"},{"subitem_subject":"hyperammonemia","subitem_subject_scheme":"Other"},{"subitem_subject":"perinatal disorder","subitem_subject_scheme":"Other"},{"subitem_subject":"先天性代謝異常症","subitem_subject_scheme":"Other"},{"subitem_subject":"ガラクトース血症","subitem_subject_scheme":"Other"},{"subitem_subject":"高アンモニア血症","subitem_subject_scheme":"Other"},{"subitem_subject":"周生期の異常","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"departmental bulletin paper","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"4) 周生期異常としての先天性代謝異常症(シンポジウム 周産期をめぐる諸問題, 第432回新潟医学会)","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"4) 周生期異常としての先天性代謝異常症(シンポジウム 周産期をめぐる諸問題, 第432回新潟医学会)"},{"subitem_title":"4) 周生期異常としての先天性代謝異常症(シンポジウム 周産期をめぐる諸問題, 第432回新潟医学会)","subitem_title_language":"en"}]},"item_type_id":"7","owner":"1","path":["456","1219"],"pubdate":{"attribute_name":"公開日","attribute_value":"2016-04-06"},"publish_date":"2016-04-06","publish_status":"0","recid":"23360","relation_version_is_last":true,"title":["4) 周生期異常としての先天性代謝異常症(シンポジウム 周産期をめぐる諸問題, 第432回新潟医学会)"],"weko_creator_id":"1","weko_shared_id":null},"updated":"2022-12-15T03:53:36.113460+00:00"}