@article{oai:niigata-u.repo.nii.ac.jp:02000774,
 author = {渡邉, 直子 and Watanabe, Naoko and 三上, 俊彦 and Mikami, Toshihiko and 小林, 正治 and Kobayashi, Tadaharu and 齋藤, 功 and Saito, Isao},
 issue = {2},
 journal = {新潟歯学会雑誌},
 month = {Dec},
 note = {Nevoid Basal Cell Carcinoma Syndrome (NBCCS) is known as Gorlin syndrome. NBCCS is a hereditary condition characterized by multiple basal cell skin cancers, jaw cysts or pits on the palms of the hands, and skeletal (bone) -related systemic changes. Particularly in the oral and maxillofacial region, multiple jaw cysts, frequently beginning in the second decade of life, are a characteristic finding of NBCCS. The patient, a 10-year 2-month-old female with NBCCS, has four keratocysts in maxilla and two in mandible. All cysts include impacted teeth. After marsupialization of the cysts, orthodontic traction and alignment of the impacted teeth was performed. At the completion of the active treatment, the shrinkage of the cysts and favorable facial growth were observed and acceptable occlusion was achieved. After 2 years of retention, stable occlusion was maintained. For the patient with NBCCS, marsupialization of the jaw cysts and following traction of the impacted teeth are highly recommended during adolescent., 基底細胞母斑症候群 Nevoid Basal Cell Carcinoma Syndrome は，GorlinとGoltzによって体系づけられた常染色体優性遺伝性疾患で，主に皮膚の多発性基底細胞母斑，基底細胞癌，顎骨の多発性角化嚢胞や，種々の骨格系統の異常を呈する症候群であるが，特に口腔領域では10代に多発する顎骨嚢胞が特徴的な疾患である。今回，複数の顎骨嚢胞，特に第二大臼歯の歯冠を含む巨大な含歯性嚢胞を有した症例に対し，10歳2か月より16歳10か月まで長期に渡って管理し，開窓術及び埋伏歯の矯正による牽引誘導を行うことで，嚢胞の縮小と良好な骨成長および咬合状態を得ることができた症例を経験したので，その治療経過と結果について報告する。また，巨大な含歯性嚢胞の埋伏歯牽引の必要性について，その効果と限界について考察するとともに，基底細胞母斑症候群の患者に対する矯正治療の適応について考察した。},
 pages = {87--95},
 title = {基底細胞母斑症候群をともなう患者の矯正歯科治療例},
 volume = {47},
 year = {2017}
}