{"created":"2022-08-30T06:35:02.116498+00:00","id":2000667,"links":{},"metadata":{"_buckets":{"deposit":"bc121da5-cc6c-448e-a68f-752508fc338f"},"_deposit":{"id":"2000667","owners":[1],"pid":{"revision_id":0,"type":"depid","value":"2000667"},"status":"published"},"_oai":{"id":"oai:niigata-u.repo.nii.ac.jp:02000667","sets":["453:456","471:537:538:1661840400705"]},"author_link":[],"item_1627361970403":{"attribute_name":"出版タイプ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_7_biblio_info_6":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2021-07","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"7","bibliographicPageEnd":"135","bibliographicPageStart":"131","bibliographicVolumeNumber":"135","bibliographic_titles":[{"bibliographic_title":"新潟医学会雑誌","bibliographic_titleLang":"ja"}]}]},"item_7_description_4":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"【症例】8歳男児．8歳9か月時に複視が出現し，その78日後，啼泣後に目の周囲に点状出血を認めた．精査の結果，重症筋無力症と免疫性血小板減少症の合併と診断した．臨床症状は眼筋症状のみだったが，鼻筋の誘発筋電図でwaningを認めたことより，潜在全身型の重症筋無力症と診断した．眼瞼下垂症状が軽微であったこと，重症筋無力症と免疫性血小板減少症の合併は稀で小児の報告例は1例のみであることから診断に苦慮した．入院11日目よりプレドニゾロンの内服を開始し，漸増した．プレドニゾロンの漸増に伴い，血小板減少は改善した．眼瞼下垂と複視も改善傾向となったが，寛解は得られなかったため，入院32日目からステロイドパルス療法を1クール行った．ステロイドパルス療法後，眼瞼下垂と複視は消失した．プレドニゾロンの内服を継続し，入院40日目に退院した．退院後は症状の再燃なく経過し，プレドニゾロンを漸減・終了した．【結語】重症筋無力症と免疫性血小板減少症の合併例は報告が少なく，確立された有効な治療はない．胸腺摘除の報告が多いが，小児期発症の場合，ステロイド治療が有効である．今後のより良い診療のためには，報告の蓄積が必要である．","subitem_description_language":"ja","subitem_description_type":"Abstract"}]},"item_7_publisher_7":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"新潟医学会","subitem_publisher_language":"ja"}]},"item_7_source_id_11":{"attribute_name":"書誌レコードID","attribute_value_mlt":[{"subitem_source_identifier":"AN00182415","subitem_source_identifier_type":"NCID"}]},"item_7_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"0029-0440","subitem_source_identifier_type":"PISSN"}]},"item_access_right":{"attribute_name":"アクセス権","attribute_value_mlt":[{"subitem_access_right":"open access","subitem_access_right_uri":"http://purl.org/coar/access_right/c_abf2"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"佐藤, 大祐","creatorNameLang":"ja"},{"creatorName":"Sato, Daisuke","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"今村, 勝","creatorNameLang":"ja"},{"creatorName":"Imamura, Masaru","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"大橋, 伯","creatorNameLang":"ja"},{"creatorName":"Ohashi, Tsukasa","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"齋藤, 昭彦","creatorNameLang":"ja"},{"creatorName":"Saitoh, Akihiko","creatorNameLang":"en"}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_access","date":[{"dateType":"Available","dateValue":"2022-08-30"}],"displaytype":"detail","filename":"135(7)_131-135.pdf","filesize":[{"value":"781KB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"objectType":"fulltext","url":"https://niigata-u.repo.nii.ac.jp/record/2000667/files/135(7)_131-135.pdf"},"version_id":"659f7dd2-4f41-4f85-a9bf-444d82bc6bbc"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"重症筋無力症","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"免疫性血小板減少症","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"ステロイド","subitem_subject_language":"ja","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"departmental bulletin paper","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"重症筋無力症と免疫性血小板減少症を合併した男児例","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"重症筋無力症と免疫性血小板減少症を合併した男児例","subitem_title_language":"ja"},{"subitem_title":"A Male Case of Myasthenia Gravis with Immune Thrombocytopenia","subitem_title_language":"en"}]},"item_type_id":"7","owner":"1","path":["456","1661840400705"],"pubdate":{"attribute_name":"PubDate","attribute_value":"2022-08-30"},"publish_date":"2022-08-30","publish_status":"0","recid":"2000667","relation_version_is_last":true,"title":["重症筋無力症と免疫性血小板減少症を合併した男児例"],"weko_creator_id":"1","weko_shared_id":-1},"updated":"2022-12-15T04:36:00.629096+00:00"}